Cystic fibrosis is a chronic, progressive and debilitating disease that affects the lungs, intestines, liver, and pancreas. Cystic fibrosis is caused ...more »
Cystic Fibrosis is listed as a "rare disease" by the Office of
Rare Diseases (ORD) of the National Institutes of Health
(NIH). This means that Cystic Fibrosis, or a subtype of Cystic Fibrosis,
affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)
Ophanet, a consortium of European partners,
currently defines a condition rare when it affects 1 person per 2,000.
They list Cystic Fibrosis as a "rare disease".
Source - Orphanet
Types of Cystic Fibrosis:
Broader types of Cystic Fibrosis:
Prevalance of Cystic Fibrosis: 1 per 31,000 Asian American newborns suffer from cystic fibrosis in the US, genetics Home Reference website
Prevalance Rate of Cystic Fibrosis: approx 1 in 31,000 or 0.00% or 8,774 people in USA [about data]
Incidence (annual) of Cystic Fibrosis: 2,500 babies annually USA; 1 in 3,000 Caucasian babies
Incidence Rate of Cystic Fibrosis: approx 1 in 108,800 or 0.00% or 2,500 people in USA [about data]
Prevalance of Cystic Fibrosis:
Every year, 1,000 children with cystic fibrosis
(CF) are born in the United States. One in 3,000 Caucasian babies have the
disorder, making CF one of the most common lethal genetic diseases in
Caucasians. Overall, there are 30,000 Americans with CF, and an estimated
8 million people carry one copy of the defective gene that causes the
disease.
(Source: excerpt from Cystic Fibrosis Research Directions: NIDDK)
Patient Profile for Cystic Fibrosis: Symptoms usually within 1 year; rarely symptoms wait till adolescence; mostly affected from birth.
Race Profile for Cystic Fibrosis: Mostly caucasian
Prognosis of Cystic Fibrosis: The predicted median age of survival for a person with CF is 37 years. However, with the continuous introduction of many new treatments, the life expectancy of a person with CF is increasing to ages as high as 40 or 50. Lung transplantation is often necessary as CF worsens
Complications of Cystic Fibrosis:
see complications of Cystic Fibrosis
Prognosis of Cystic Fibrosis:
Improved therapy has transformed CF from a disease characterized by
death in early childhood to a chronic illness, with most patients living
to adulthood. But despite this progress, there still is no cure for the
disease and most patients eventually succumb to infections of the airways
and lung failure.
(Source: excerpt from Cystic Fibrosis Research Directions: NIDDK)
...
On the average, individuals with CF have a lifespan of approximately 30 years.
(Source: excerpt from NHLBI, Facts About Cystic Fibrosis: NHLBI)
Deaths for Cystic Fibrosis: 485 deaths (NHLBI 1999)
Causes of Cystic Fibrosis: see causes of Cystic Fibrosis
Causes of Cystic Fibrosis:
CF affects tissues that produce mucus
secretions, such as the airway, the gastrointestinal tract, the ducts of
the pancreas, the bile ducts of the liver and the male urogenital tract.
Normal mucus forms a gel-like barrier that plays an important role in
protecting the cells lining the inside surfaces of these tissues. In the
lung, mucus also transports dust and other particles out of the airway and
helps to prevent infection. CF alters the chemical properties of mucus;
instead of protecting tissues from harm, the abnormal mucus obstructs the
ducts and airways, causing tissue damage.
(Source: excerpt from Cystic Fibrosis Research Directions: NIDDK)
Risk factors for Cystic Fibrosis:
see
risk factors for Cystic Fibrosis
Symptoms of Cystic Fibrosis: see symptoms of Cystic Fibrosis
Complications of Cystic Fibrosis: see complications of Cystic Fibrosis
Onset of Cystic Fibrosis: Symptoms of CF appear in infancy and childhood
Inheritance:
see inheritance of Cystic Fibrosis
Inheritance of genetic conditions: see details in inheritance of genetic diseases.
Diagnostic testing: see tests for Cystic Fibrosis.
Misdiagnosis: see misdiagnosis and Cystic Fibrosis.
Treatments for Cystic Fibrosis:
see treatments for Cystic Fibrosis
Alternative treatments for Cystic Fibrosis:
see alternative treatments for Cystic Fibrosis
Prevention of Cystic Fibrosis:
see prevention of Cystic Fibrosis
Research for Cystic Fibrosis:
see research for Cystic Fibrosis
Hospitalizations for Cystic Fibrosis: 12,000 (NHLBI 1999)
Hospitalization statistics for Cystic Fibrosis:
The following are statistics from various sources about hospitalizations and Cystic Fibrosis:
Organs and body systems related to Cystic Fibrosis include:
Main name of condition: Cystic Fibrosis
Class of Condition for Cystic Fibrosis: genetic autosomal recessive
CF, cystic fibrosis of pancreas, fibrocystic disease of pancreas, mucoviscidosis, Mucovoidosis
Mucoviscidosis
Source - Diseases Database
CF, Fibrocystic disease of the pancreas, Pancreatic fibrosis, Mucoviscidosis
Source - WordNet 2.1
CF, Mucoviscidosis
Source - Office of Rare Diseases (ORD) of the National Institutes of Health (NIH)
Research the causes of these diseases that are similar to, or related to, Cystic Fibrosis:
Tools & Services:
Medical Articles:
Search Specialists by State and City
By using this site you agree to our Terms of Use. Information provided on this site is for informational purposes only; it is not intended as a substitute for advice from your own medical team. The information on this site is not to be used for diagnosing or treating any health concerns you may have - please contact your physician or health care professional for all your medical needs. Please see our Terms of Use.
Copyright © 2011 Health Grades Inc. All rights reserved. Last Update: 7 May, 2013 (4:32)
