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What is Lymphangioleiomyomatosis?

What is Lymphangioleiomyomatosis?

  • Lymphangioleiomyomatosis: A very rare progressive disease where an unusual type of muscle cell (smooth muscle) infiltrates the lungs which eventually obstructs the flow of air through the lungs. The cause is unknown and generally occurs in women of child bearing age.
  • Lymphangioleiomyomatosis: rare lung disorder of unknown etiology mostly in women of childbearing age; proliferation of atypical smooth muscle cells in lungs, airways, blood and lymph vessels causing obstruction; symptoms include dyspnea and pneumothorax.
    Source - Diseases Database

Ophanet, a consortium of European partners, currently defines a condition rare when it affects 1 person per 2,000. They list Lymphangioleiomyomatosis as a "rare disease".
Source - Orphanet

Lymphangioleiomyomatosis: Introduction

Types of Lymphangioleiomyomatosis:

Broader types of Lymphangioleiomyomatosis:

How many people get Lymphangioleiomyomatosis?

Prevalance of Lymphangioleiomyomatosis: Several hundred people in the USA (NHLBI)
Prevalance of Lymphangioleiomyomatosis: The precise number of people who have LAM is not known. It has been estimated that there may be up to several hundred women in the United States with the disease. (Source: excerpt from NHLBI, Facts About Lymphangioleiomyomatosis (LAM): NHLBI)

Who gets Lymphangioleiomyomatosis?

Patient Profile for Lymphangioleiomyomatosis: Typically young adult women.

Profile for Lymphangioleiomyomatosis: LAM affects almost exclusively women of childbearing age, although several cases have been reported in which the disease was thought to have developed after menopause. The international literature also includes reports of a few cases in men. (Source: excerpt from NHLBI, Facts About Lymphangioleiomyomatosis (LAM): NHLBI)

Gender Profile for Lymphangioleiomyomatosis: Mostly women. Men are rare.

Gender Ratio for Lymphangioleiomyomatosis: females only

How serious is Lymphangioleiomyomatosis?

Prognosis of Lymphangioleiomyomatosis: Poor. Commonly death within 10 years.
Complications of Lymphangioleiomyomatosis: see complications of Lymphangioleiomyomatosis

What causes Lymphangioleiomyomatosis?

Causes of Lymphangioleiomyomatosis: see causes of Lymphangioleiomyomatosis

What are the symptoms of Lymphangioleiomyomatosis?

Symptoms of Lymphangioleiomyomatosis: see symptoms of Lymphangioleiomyomatosis

Complications of Lymphangioleiomyomatosis: see complications of Lymphangioleiomyomatosis

Lymphangioleiomyomatosis: Testing

Diagnostic testing: see tests for Lymphangioleiomyomatosis.

Misdiagnosis: see misdiagnosis and Lymphangioleiomyomatosis.

How is it treated?

Doctors and Medical Specialists for Lymphangioleiomyomatosis: Pulmonologist ; see also doctors and medical specialists for Lymphangioleiomyomatosis.
Treatments for Lymphangioleiomyomatosis: see treatments for Lymphangioleiomyomatosis

Organs Affected by Lymphangioleiomyomatosis:

Organs and body systems related to Lymphangioleiomyomatosis include:

Name and Aliases of Lymphangioleiomyomatosis

Main name of condition: Lymphangioleiomyomatosis

Other names or spellings for Lymphangioleiomyomatosis:

LAM, Pulmonary Lymphangioleiomyomatosis, lymphangiomyomatosis, pulmonary lymphangiomyomatosis

Pulmonary lymphangioleiomyomatosis Source - Diseases Database

Lymphangioleiomyomatosis: Related Conditions

Research the causes of these diseases that are similar to, or related to, Lymphangioleiomyomatosis:

 

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