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Articles » NINDS Ramsay Hunt Syndrome Type I Information Page: NINDS
 

NINDS Ramsay Hunt Syndrome Type I Information Page: NINDS

Article title: NINDS Ramsay Hunt Syndrome Type I Information Page: NINDS

Main condition: Ramsay Hunt Syndrome Type I

Conditions: Ramsay Hunt Syndrome Type I


What is Ramsey Hunt Syndrome Type I?
Ramsay Hunt syndrome Type I, also called dyssynergia cerebellaris myoclonica, refers to a collection of rare, degenerative, neurological disorders characterized by epilepsy, cognitive impairment, myoclonus, and progressive ataxia. Symptoms include seizures, tremor, and reduced muscle coordination. Onset of the disorder generally occurs in early adulthood. Tremor may begin in one extremity and later spread to involve the entire voluntary muscular system. Arms are usually more affected than legs. Some of the cases are due to mitochondrial abnormalities.

Is there any treatment?
Treatment of Ramsay Hunt Type I is symptomatic. Myoclonus and seizures may be treated with drugs like valproate.

What is the prognosis?
The progression of the disorder is usually 10 years or longer.

What research is being done?
The NINDS supports a broad range of research on neurodegenerative disorders such as Ramsay Hunt syndrome Type I. The goals of this research are to find ways to prevent, treat, and cure these disorders.

 Organizations

National Ataxia Foundation (NAF)
2600 Fernbrook Lane
Suite 119
Minneapolis, MN 55447-4752
naf@ataxia.org
https://www.ataxia.org/
Tel: 763-553-0020
Fax: 763-553-0167

National Organization for Rare Disorders (NORD)
P.O. Box 8923
(100 Route 37)
New Fairfield, CT 06812-8923
orphan@rarediseases.org
https://www.rarediseases.org/
Tel: 203-746-6518 800-999-NORD (6673)
Fax: 203-746-6481

National Institute on Deafness and Other Communication Disorders (NIDCD)
National Institutes of Health
Bldg. 31, Rm. 3C35
Bethesda, MD 20892-2320
nidcdinfo@nidcd.nih.gov
https://www.nidcd.nih.gov/
Tel: 301-496-7243 TTD/TTY: 301-241-1055

This fact sheet is in the public domain. You may copy it.Provided by:
The National Institute of Neurological Disorders and Stroke
National Institutes of Health
Bethesda, MD 20892


 

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