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Diseases » Jensen syndrome » Summary
 

What is Jensen syndrome?

What is Jensen syndrome?

  • Jensen syndrome: A rare genetic disorder characterized by degeneration of the optic nerve (causing impaired vision), deafness due to nerve damage and dementia due to calcification of the central nervous system. Death usually results by about the age of 40 with extensive calcification of all parts of the nervous system.

Jensen syndrome is listed as a "rare disease" by the Office of Rare Diseases (ORD) of the National Institutes of Health (NIH). This means that Jensen syndrome, or a subtype of Jensen syndrome, affects less than 200,000 people in the US population.
Source - National Institutes of Health (NIH)

Ophanet, a consortium of European partners, currently defines a condition rare when it affects 1 person per 2,000. They list Jensen syndrome as a "rare disease".
Source - Orphanet

Jensen syndrome: Introduction

Types of Jensen syndrome:

Broader types of Jensen syndrome:

Who gets Jensen syndrome?

Gender Ratio for Jensen syndrome: male predominance

How serious is Jensen syndrome?

Prognosis of Jensen syndrome: The prognosis is poor with reported cases resulting in death at about the age of 40 years. Deafness is present at birth, vision loss starts during adolescence and results in blindness and dementia starts in adulthood.
Complications of Jensen syndrome: see complications of Jensen syndrome

What causes Jensen syndrome?

Causes of Jensen syndrome: see causes of Jensen syndrome

What are the symptoms of Jensen syndrome?

Symptoms of Jensen syndrome: see symptoms of Jensen syndrome

Complications of Jensen syndrome: see complications of Jensen syndrome

Onset of Jensen syndrome: Deafness was present at birth, vision loss starts during adolescence and dementia starts in adulthood.

Jensen syndrome: Testing

Diagnostic testing: see tests for Jensen syndrome.

Misdiagnosis: see misdiagnosis and Jensen syndrome.

How is it treated?

Doctors and Medical Specialists for Jensen syndrome: Medical Geneticist ; see also doctors and medical specialists for Jensen syndrome.
Treatments for Jensen syndrome: see treatments for Jensen syndrome
Research for Jensen syndrome: see research for Jensen syndrome

Name and Aliases of Jensen syndrome

Main name of condition: Jensen syndrome

Other names or spellings for Jensen syndrome:

optoacoustic nerve atrophy [dementia], Opticoacoustic nerve atrophy [dementia], Opticoacustic nerve atrophy with dementia, Nerve deafness optic nerve atrophy, and dementia, Syndrome of opticoacoustic nerve atrophy with dementia

Nerve deafness optic nerve atrophy, and dementia, Opticoacustic nerve atrophy with dementia, Syndrome of opticoacoustic nerve atrophy with dementia
Source - Office of Rare Diseases (ORD) of the National Institutes of Health (NIH)

Jensen syndrome: Related Conditions

Research the causes of these diseases that are similar to, or related to, Jensen syndrome:

 

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